Table 2.

Prevalence for the involvement of each organ/system at first consultation in childhood-onset granulomatosis with polyangiitis and microscopic polyangiitis

Organ/system	ENT	Systemic	Renal	Lower respiratory tract	Musculoskeletal	Cutaneous	Ocular	Gastrointestinal	Neurological	Cardiovascular
GPA
Pooled prevalence	82	73	65	61	55	44	24	19	13	4
95 % CI	78–87	55–88	49–79	48–74	43–67	32–57	15–34	10–30	9–17	1–9
I2	26	88	84	77	72	75	64	72	15	61
MPA
Pooled prevalence	3	79	94	37	57	44	7	28	18	2
95 % CI	1–7	65–90	89–97	24–52	27–86	27–61	3–11	17–41	7–34	0–5
I2	0	64	47	67	89	73	0	55	72	0