Table 1.
Patient | Visual Acuity* |
Optic Disc Fibrosis (bilateral) |
Posterior Pole (Macular) Changes |
Peripheral Retinal Changes | Other |
---|---|---|---|---|---|
1 | RE: 20/16 LE: 20/16 |
Present | Vascular tortuosity with dilated veins Few arteriolar narrowing and subtle retinal pigmentary changes |
Bilateral peripheral scattered retinal pigment epithelial (RPE) changes |
|
2 | RE: 20/32 LE: 20/25 |
Present | Absent | Absent | Bilateral cataract (posterior subcapsular) |
3◊ | RE: 20/25 LE: 20/25 |
Present | Absent | Bilateral peripheral retinal neovascularization present; LE: single hemangioblastoma-like lesion similar to VHL in the inferior temporal retina |
Myelinated nerve fiber layer in LE |
4 | RE: 20/20 LE: 20/20 |
Present | Absent | Bilateral temporal vasculature anomalies similar to familial exudative vitreoretinopathy / retinopathy of prematurity like appearance with U-turning blood vessels |
|
5◊ | RE: 20/25 LE: 20/32 |
Present | Bilateral macular edema** with retinal hard exudate |
Absent | Bilateral enlarged blind spot |
6◊ | RE: 20/20 LE: 20/63 |
Present | Absent | Absent | LE with optic nerve head drusen and amblyopia |
7◊ | RE: 20/250 LE: 20/20 |
Present | Macular edema*** with hard exudate RE only |
Absent |
Visual Acuity: measured on a LogMAR Visual Acuity Chart (Early Treatment Diabetic Retinopathy Study visual acuity chart) at 4 meters, best corrected
Intravitreal injection of Ranibizumab was administered
Intravitreal injection of Bevacizumab was administered
see also Pacak et al. 2014
Abbreviations: LE=left eye; RE=right eye; VHL=von Hippel-Lindau;