Table 2. Components of the revised Ghent nosology in patients with MFS.

	Events/available data	%
Ao (Z score ≥2)	303/342	88.6
Ectopia lentis	163/296	55.1
FBN1 gene mutation	141/157*	89.8
Systemic score ≥7	217/294	73.8
Family history of MFS	97/218	44.5

^*Number of available data among the probands. ^†Number of probands. MFS: Marfan syndrome, Ao: aortic diameter at the sinus of Valsalva above indicated Z-score or aortic root dissection, FBN1: Fibrillin-1