Table 1.

Patient demographics and surgical experience

Variable	Control (N=55)	22q11.2 DS (N=36)	p-value
Demographic Information
Age, days (median, range)	120 (5–4588)	55 (6–4320)	0.73
Gender, Male (N, %)	33 (60%)	16 (44%)	0.20
Weight, kg (median, range)	5.4 (1.9–86.0)	3.9 (2.1–33.6)	0.25
Cardiac anatomy diagnosis (N, %)			0.88
Tetralogy of Fallot-pulmonary stenosis	19 (35%)	11 (31%)
Tetralogy of Fallot-pulmonary atresia	5 (9%)	3 (8%)
Tetralogy of Fallot-pulmonary atresia and MAPCAs	4 (7%)	2 (6%)
Truncus Arteriosus	7 (13%)	9 (25%)
Truncus Arteriosus with Interrupted Aortic Arch	2 (3%)	0 (0%)
Interrupted Aortic Arch	7 (13%)	5 (13%)
Ventricular Septal Defect	8 (15%)	4 (11%)
Other	3 (5%)	2 (6%)
Surgical Information
Procedure (N, %)			0.80
Tetralogy of Fallot, RV-PA conduit	6 (11%)	3 (8%)
Tetralogy of Fallot, transannular patch	16 (29%)	7 (20%)
Truncus Arteriosus repair	7 (13%)	9 (25%)
Interrupted Aortic Arch repair	7 (13%)	5 (14%)
PA-VSD repair	6 (11%)	4 (11%)
VSD repair	8 (14%)	4 (11%)
Other	5 (9%)	4 (11%)
Surgeon (N, %)			0.34
Surgeon A	26 (47%)	19 (53%)
Surgeon B	20 (37%)	12 (33%)
Surgeon C	4 (7%)	3 (8%)
Surgeon D	2 (4%)	0 (0%)
Surgeon E	0 (0%)	2 (6%)
Surgeon F	3 (5%)	0 (0%)
Prime information
Priming product (N, %)			0.59
Whole blood	50 (91%)	33 (92%)
Packed red blood cells and fresh frozen plasma	3 (5%)	3 (8%)
Clear prime only	2 (4%)	0 (0%)
Prime amount, ml/kg (median, range)	72 (16–184)	97 (39–190)	0.16
Cardiopulmonary bypass time, minutes (median, range)	152 (61–632)	172 (52–549)	0.21
Lowest temperature during surgery, °C (median, range)	27.6 (16.3–33.4)	27.6 (15.1–34.3)	0.85

MAPCAs = major aortopulmonary collateral arteries; PA-VSD = pulmonary atresia with ventricular septal defect; RV-PA = right ventricle to pulmonary artery