Table 1.
Classification of Histiocytic disorders.
| HD type | Examples |
|---|---|
| L group | LCH Indeterminate cell histiocytosis ECD Mixed ECD and LCH |
| C group | Cutaneous non-LCH histiocytoses Cutaneous non-LCH histiocytoses with a major systemic component |
| M group | Primary malignant histiocytosis Secondary malignant histiocytosis |
| R group | Nodal RDD Extranodal RDD Neoplasia-associated RDD Immune disease-associated RDD |
| H group | Primary HLH Secondary HLH |
ECD, Erdheim–Chester disease; HD, histiocytic disorder; HLH, haemophagocytic lymphohistiocytosis; LCH, Langerhans cell histiocytosis; RDD, Rosai–Dorfman disease.