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. 2016 Jul 19;89(1065):20160221. doi: 10.1259/bjr.20160221

Table 1.

Classification of Histiocytic disorders.

HD type Examples
L group LCH
Indeterminate cell histiocytosis
ECD
Mixed ECD and LCH
C group Cutaneous non-LCH histiocytoses
Cutaneous non-LCH histiocytoses with a major systemic component
M group Primary malignant histiocytosis
Secondary malignant histiocytosis
R group Nodal RDD
Extranodal RDD
Neoplasia-associated RDD
Immune disease-associated RDD
H group Primary HLH
Secondary HLH

ECD, Erdheim–Chester disease; HD, histiocytic disorder; HLH, haemophagocytic lymphohistiocytosis; LCH, Langerhans cell histiocytosis; RDD, Rosai–Dorfman disease.