Table 2.
Clinical characteristics and diagnosis of 12 patients
| Clinical characteristics | n = 12 |
| Male/female | 5/7 |
| Age at initial visit [years] | 62 (47–75) |
| Acute onset/chronic onset | 8/4 |
| Smoking status (current or former/never smoker) | 6/6 |
| Serological findings (reference value) | n = 12 |
| CK [U/L] (62–287) | 140 (17–672) |
| LDH [U/L] (70–139) | 252 (212–337) |
| ESR [mm/h] (2–10) | 38 (17–116) |
| CRP [mg/dl] (0–0.1) | 0.63 (0.03–1.79) |
| KL-6 [U/ml] (0–500) | 991 (514–3208) |
| SP-D [ng/ml] (0–110) | 232.3 (56.1–723.1) |
| PaO2 [Torr] (74–108) | 71.5 (53.0–84.5) |
| Pulmonary functions | n = 11 |
| FVC % predicted [%] | 71.5 (42.4–86.1) |
| DLCO % predicted [%] | 66.1 (56.0–112.2) |
Data are presented as n, or median (range)
CK: Creatine kinase, LDH: Lactate dehydrogenase, ESR: Erythrocyte sedimentation rate, CRP: C-reactive protein, KL-6: Klebs von den lungen-6, SP-D: Surfactant protein D, PaO 2: Arterial oxygen pressure, FVC: Forced vital capacity, DL CO: Diffusion capacity for carbon monoxide