Table 1.
Patients' information.
| Patient | Gender | Age at diagnosis (years) |
Location | Genetic background | Tumor size (cm) | Urinary norepinephrine (μg/24 h) |
Urinary epinephrine (μg/24 h) |
Urinary dopamine (μg/24 h) |
|---|---|---|---|---|---|---|---|---|
| N1 | F | 72 | Adrenal | N | 3.0 | 22.4 | 3.7 | 156.6 |
| N2 | F | 57 | Adrenal | N | 4.0 | 19.3 | 1.9 | 181.3 |
| N3 | F | 40 | Adrenal | N | 4.7 | 16.9 | 1.5 | 67.9 |
| N4 | M | 59 | Adrenal | N | 6.3 | 100.9 | 2.8 | 140.1 |
| N5 | F | 26 | Adrenal | N | 4.0 | 20.4 | 2.3 | 135.7 |
| N6 | M | 40 | Adrenal | N | 5.0 | 177.1 | 1.1 | 256.6 |
| D1 | F | 47 | Adrenal | SDHD | 8.0 | 215.0 | 2.8 | 311.1 |
| B1 | M | 26 | Retroperitoneal | SDHB | 5.0 | 138.9 | 2.3 | 1046.5 |
| B2 | M | 62 | Adrenal | SDHB | 3.7 | 15.4 | 1.9 | 177.4 |
| B3 | F | 48 | Retroperitoneal | SDHB | 9.0 | 121.4 | 1.8 | 147.1 |
| V1 | M | 21 | Adrenal | VHL | 7.5 | 937.5 | 2.3 | 127.3 |
| V2 | F | 34 | Adrenal and retroperitoneal |
VHL | 4.5 (adrenal)/4.0 (retroperitoneal) | 239.2 | 13.3 | 153.8 |
| V3 | M | 8 | Adrenal | VHL | 4.0 | 214.1 | 4.6 | 98.3 |
| R1 | F | 33 | Adrenal | RET | 3.7 | 13.9 | 2.7 | 237.6 |
| R2 | F | 30 | Adrenal | RET | 5.0 | 21.2 | 5.3 | 456.2 |
| R3 | M | 49 | Adrenal | RET | 2.4 | 20.8 | 3.5 | 326.3 |
| R4 | F | 27 | Adrenal | RET | 7.3 | 20.5 | 3.0 | 163.2 |
| R5 | F | 45 | Adrenal | RET | 6.9 | 315.3 | 2.6 | 268.8 |
N: PPGL without gene mutation of SDHB, SDHC, SDHD, VHL, and RET; M: male; F: female. Reference range: urinary norepinephrine 16.7–40.7 μg/24 h; urinary epinephrine 1.7–6.4 μg/24 h; urinary dopamine 120.9–330.6 μg/24 h.