Table 2.
Reported cases of extrarenal teratoid Wilms' tumor. Summary of the 5 other cases of extrarenal teratoid Wilms' tumor.
| First Author, year | Age in years | Location | Presenting symptoms | Treatment | Tumor traits (dimensions) | Presence of anaplasia? | Outcome | Follow-up |
|---|---|---|---|---|---|---|---|---|
| Sex | ||||||||
| Pawel et al. (1998) | 7/M | Partly cystic ureteropelvic mass | 1 week of abdominal pain | Exploratory laparotomy + excision of retroperitoneal mass + vincristine & actinomycin-D × 18 weeks | 8 × 4 cm (spherical) | No | No recurrence | 18 months |
| Song et al. (2010) | 13/F | Partly cystic mass in vagina originating from uterine cervix (no mass in endometrial cavity) | vaginal spotting | Removal of vaginal mass + vincristine, cyclophosphamide, & actinomycin D × 6 months | 6 × 5 cm | No | No recurrence | 84 months |
| Song et al. (2010) | 1 day/F | Multilobulated sacrococcygeal mass | Detected on ultrasound during prenatal care | Excision of mass on Day 2 of life + vincristine & actinomycin-D × 6 months | 15 × 15 cm | No | No recurrence | 29 months |
| Chowhan et al. (2011) | 1.3/M | Retroperitoneal mass below left kidney | Growing abdominal distention | Exploratory laparotomy with excision of mass + vincristine & actinomycin-D × 6 months | 6.6 × 5.9 cm | No | No recurrence | 6 months |
| Baskaran (2012) | 3/M | Right sided solid abdominal mass | Abdominal distention due to mass | Exploratory laparotomy with excision of mass | 10 × 11 cm | No | No recurrence | 12 months |