Table 5. Inflammatory diseases in HEDS patients.
| Diagnosis | NWU | LWU | CWU | |
|---|---|---|---|---|
| Psoriasis | 6 [2.5%] | 1 [2.0%] | 15 [17.1%] | |
| Ankylosing spondylitis | 0 | 2 [3.9%] | 9 [10.2%] | |
| Psoriatic arthritis | w/o erosions | 0 | 0 | 8 [9.1%] |
| w/erosions | 0 | 0 | 3 [3.4%] | |
| Seronegative rheumatoid arthritis | w/o erosions | 0 | 2 [3.9%] | 2 [2.3%] |
| w/erosions | 0 | 0 | 1 [1.1%] | |
| Seropositive rheumatoid arthritis | w/o erosions | 0 | 1 [2.0%] | 2 [2.3%] |
| w/erosions | 0 | 0 | 1 [1.1%] | |
| Inflammatory eye disease | 0 | 0 | 4 [4.6%] | |
| Systemic lupus erythematosus | 0 | 1 [2.0%] | 2 [2.3%] | |
| Autoimmune thyroiditis | 0 | 0 | 2 [2.3%] | |
| Diffuse enthesopathy | 0 | 0 | 2 [2.3%] | |
| Juvenile inflammatory arthritis | 0 | 2 [3.9%] | 0 | |
| Undifferentiated spondyloarthropathy | 0 | 0 | 2 [2.3%] | |
| Celiac disease | 0 | 0 | 1 [1.1%] | |
| Costochondritis | 0 | 1 [2.0%] | 0 | |
| Crohn’s disease | 0 | 0 | 1 [1.1%] | |
| Erythema nodosum | 0 | 0 | 1 [1.1%] | |
| Kawasaki disease | 1 [0.4%] | 0 | 0 | |
| Mixed connective tissue disease | 0 | 0 | 1 [1.1%] | |
| Pernicious anemia | 0 | 0 | 1 [1.1%] | |
| Polymyalgia rheumatica | 0 | 1 [2.0%] | 0 | |
| Sacroiliitis | 0 | 0 | 1 [1.1%] | |
| Sjogren’s disease | 0 | 0 | 1 [1.1%] | |
| Seronegative tenosynovitis | 0 | 0 | 1 [1.1%] | |
| TRAPS | 0 | 0 | 1 [1.1%] | |