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. 2017 Jan 10;12(1):e0169783. doi: 10.1371/journal.pone.0169783

Table 2. Clinical Profiles of 14 Patients without SWC.

Patient number Peak TSB (μmol/L) Gender Gestational age (d) Onset Time(d) Birth weight (g) Diagnosis MRI (yes/no) Seizure (yes/no) BAEP (grade) EEG (grade) Follow-up
1 996.2 M 40W 4 2850 G-6-PD deficiency Ni Y 3 3 CP
2 737.0 M 35W+6 4 3100 G-6-PD deficiency Y Y 5 3 MR, API
3 650.4 M 37W+5 3 3200 G-6-PD deficiency Y Y 5 3 LOST
4 645.3 F 38W 4 2980 G-6-PD deficiency Ni Y 5 3 Following-up
5 640.2 M 39W+2 1 2500 G-6-PD deficiency Y Y 5 3 LOST
6 616.9 M 40W+1 1 2800 G-6-PD deficiency Y Y 5 3 MR, API
7 600.0 M 40W+5 2 2700 G-6-PD deficiency N Y 3 3 LOST
8 591.2 F 38W+2 3 2790 BI Y Y 5 3 MR, API
9 483.9 F 37W+2 0 2700 unknown N Y 5 3 API
10 550.0 M 37W+1 3 3000 G-6-PD deficiency Ni N Ni 4 DEAD
11 693.3 M 37W+2 3 3090 G-6-PD deficiency Ni N Ni 4 DEAD
12 532.0 F 37W 3 2700 unknown Y Y 5 4 Following-up
13 700.0 F 37W+5 1 2670 unknown N Y 5 4 CP
14 514.2 M 37W+2 0 2580 unknown Ni N 4 4 LOST

BI: Blood group incompatibility; MRI: Typical MRI in GP area (GP, globi pallidi); T2WI, T2-weighted images, Ni, Not implemented; EEG, Grade 1–4 represented normal, mild abnormal, moderate abnormal and severe abnormal EEG respectively; BAEP, brain-stem auditory evoked potential; Grade 1–5 represented normal, mild abnormal, moderate abnormal, severe abnormal and no response respectively; CP, cerebral palsy; MR: mental retardation; API, Auditory pathway injury;

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