Fig. 1.

Clinical and radiological features of our patient. a Coronal FLAIR-T2 MRI showing generalized cerebral atrophy and ex vacuo ventricular dilation. b Sagittal T1-weighted MRI showing midline cerebellar atrophy. c Axial T2-weighted MRI showing cerebellar and pontine atrophy with dilation of the fourth ventricle and punctate bilateral high signal lesions at the base of the middle cerebellar peduncles (arrow). d Photograph of the patient showing severe bilateral edema of the lower limbs. e Improvement of the edema after albumin infusion and compression treatment