Table 1.

Pancreatic malformations 7

Anomalies	Anatomical disorder	Frequency
Pancreas divisum	Fusion failure between dorsal and ventral buds, mainly ducts: Wirsung and Santorini with two distinct draining orifices	4–14%
Annular pancreas	Rotation failure of ventral bud: pancreatic tissue enveloping the second part of the duodenum	1/20,000
Ectopic pancreas	Pancreatic tissue arising elsewhere in the GI tract (gastric antrum, jejunum, duodenum, appendix, Meckel's diverticulum, etc.) with no vascular or anatomical continuity with the pancreas	1–15%
Accessory pancreatic lobe	Pancreatic tissue, arising from the pancreas, containing an aberrant pancreatic duct, in continuity with the main pancreatic duct and in most often with a gastric duplication cyst	Extremely rare
Agenesis of the dorsal pancreas	Complete: Anterior head, body, tail, Santorini's duct, and minor papilla are absent Partial: Some pancreatic tissue is present, and Santorini's duct and minor papilla remnants are present	Extremely rare