Table 2.

Cases of agenesis of the dorsal pancreas with associated pancreatic tumors found in the literature

Case	Age/gender	Presentation	Tumor	Management	Outcome
Matsusue et al. 11	53/F	Abdominal pain, weight loss, hyperglycemia	Adenocarcinoma	Total pancreatectomy, lymph node dissection, Roux‐en‐Y gastrojejunostomy, hepaticojejunostomy	No recurrence
Ulusan et al. 12	72/M	Abdominal pain, jaundice, hyperglycemia	Adenocarcinoma	Hepaticojejunostomy, cholecystectomy + chemotherapy	Unknown
Ulusan et al. 13	49/F	Abdominal pain, hyperglycemia	Solid pseudopapillary tumor	Whipple procedure	No recurrence
Nakamura et al. 14	28/F	Asymptomatic	Solid papillary tumor	Partial pancreatic head resection	No recurrence
Rittenhouse et al. 15	37/F	Abdominal pain, hyperglycemia	Ductal adenocarcinoma	Pancreatic head and uncinate process resection, hepaticojejunostomy, duodenojejunostomy + chemotherapy	Death (at 17 month)
Rittenhouse et al. 15	59/F	Weight loss	Ductal adenocarcinoma	Pancreatic head and uncinate process resection, hepaticojejunostomy, duodenojejunostomy + chemotherapy + radiation	No recurrence (at 38 month)
Rittenhouse et al. 15	68/M	Elevated LFTs	Ductal adenocarcinoma	Pancreatic head and uncinate process resection, hepaticojejunostomy, duodenojejunostomy + chemotherapy + radiation	No recurrence (at 38 month)
Sakpal et al. 16	49/M	Fatigue, diarrhea, weight loss	IPMN with well differentiated, invasive, mucinous adenocarcinoma	Whipple procedure with total pancreatectomy, lymph node dissection	No recurrence (at 6 week)
Sannappa et al. 17	51/F	Painless jaundice	Adenocarcinoma	Whipple procedure with total pancreatectomy, lymph node dissection + chemotherapy	Unknown
Our case	29/M	Abdominal pain	Infiltrating, moderately differentiated mucinous adenocarcinoma + cystic teratoma	Whipple procedure (pyloric preserving) with total pancreatectomy, lymph node dissection + chemotherapy	No recurrence (at 3 month)