Table 1.
Summary of electrophysiological property of the pedigree.
| Age | symptom | Rest ECG | 3rd ICLs | Pilsicainide administration | HR | PR interval | QRS interval | QTc Bazett’s | |
|---|---|---|---|---|---|---|---|---|---|
| Proband | 13 y.o. | SSS, VF | Saddle back | Coved | n.d. | 60 bpm atrial pacing | 262 ms | 125 ms | 436 ms |
| Mother | 46 y.o. | None | Normal | Coved | n.d. | 68 bpm | 215 ms | 128 ms | 445 ms |
| Sister | 19 y.o. | None | Normal | Normal | Coved | 57 bpm (44 bpm) | 188 ms (214 ms) | 112 ms (148 ms) | 424 ms (418 ms) |
| Brother | 21 y.o. | None | Normal | Normal | Saddle back | 68 bpm (75 bpm) | 185 (216 ms) | 134 ms (134 ms) | 427 ms (401 ms) |
The values in the pilsicainide administration are given in parentheses.
ICL: intercostal lead, y.o.: years old, SSS: sick sinus syndrome, VF ventricular fibrillation, n.d.: not done.