Table 2.
Descriptive statistics for all upper extremity outcome measures: by total and by diagnosis type.
| Test | Measure | N | Mean | SD | SE | |
|---|---|---|---|---|---|---|
| MFM32 | DISTAL-D3 | TOTAL | 42 | 15.4 | 4.6 | .7 |
| COL6 | 22 | 17.50 | 3.57 | .76 | ||
| LAMA2 | 20 | 13.1 | 4.51 | 1.01 | ||
| MFMTOTAL | TOTAL | 42 | 46.6 | 22.9 | 3.5 | |
| COL6 | 22 | 55.27 | 23.18 | 4.94 | ||
| LAMA2 | 20 | 37.15 | 19.01 | 4.25 | ||
| Jebsen | Non-dominant (ND) | TOTAL | 42 | 228.2 | 209.4 | 32.3 |
| COL6 | 22 | 161.83 | 201.54 | 42.97 | ||
| LAMA2 | 20 | 301.25 | 197.42 | 44.14 | ||
| Dominant (D) | TOTAL | 42 | 191.6 | 209.6 | 32.3 | |
| COL6 | 22 | 128.34 | 200.30 | 42.70 | ||
| LAMA2 | 20 | 261.10 | 201.76 | 45.11 | ||
| Quest | Dissociated movements | TOTAL | 42 | 86.66 | 14.01 | 2.16 |
| COL6 | 22 | 92.00 | 11.17 | 2.38 | ||
| LAMA2 | 20 | 80.78 | 14.72 | 3.29 | ||
| Grasps | TOTAL | 42 | 88.8 | 9.82 | 1.52 | |
| COL6 | 22 | 91.25 | 7.98 | 1.70 | ||
| LAMA2 | 20 | 86.10 | 11.10 | 2.48 | ||
| Weightbearing | TOTAL | 38 | 71.09 | 16.78 | 2.72 | |
| COL6 | 19 | 65.04 | 30.58 | 6.52 | ||
| LAMA2 | 19 | 63.54 | 21.83 | 4.88 | ||
| Protective extension | TOTAL | 37 | 63.06 | 15.17 | 2.49 | |
| COL6 | 20 | 57.51 | 22.92 | 4.89 | ||
| LAMA2 | 17 | 53.40 | 27.72 | 6.20 | ||
| Myometry | Elbow flex ND | TOTAL | 42 | 20.59 | 12.30 | 1.90 |
| COL6 | 22 | 29.33 | 14.54 | 3.10 | ||
| LAMA2 | 20 | 16.40 | 14.94 | 3.34 | ||
| Elbowflex D | TOTAL | 42 | 19.77 | 12.48 | 1.93 | |
| COL6 | 22 | 30.59 | 16.10 | 3.43 | ||
| LAMA2 | 20 | 15.52 | 13.87 | 3.10 | ||
| Elbowext ND | TOTAL | 42 | 17.09 | 15.25 | 2.36 | |
| COL6 | 22 | 18.85 | 10.14 | 2.16 | ||
| LAMA2 | 20 | 9.68 | 15.66 | 3.50 | ||
| Elbowext D | TOTAL | 42 | 17.60 | 17.03 | 2.63 | |
| COL6 | 22 | 18.73 | 11.18 | 2.38 | ||
| LAMA2 | 20 | 10.00 | 13.99 | 3.13 | ||
| Goniometry | Range of motion | |||||
| Elbowext ND | TOTAL | 42 | −44.84 | 34.23 | 5.63 | |
| COL6 | 22 | −38.68 | 37.09 | 7.90 | ||
| LAMA2 | 20 | −54.00 | 29.72 | 6.65 | ||
| Elbowext D | TOTAL | 42 | −47.14 | 35.70 | 5.87 | |
| COL6 | 22 | −40.27 | 38.62 | 8.23 | ||
| LAMA2 | 20 | −55.60 | 31.30 | 7.00 | ||
| Myoset tools | Myogrip | TOTAL | 42 | 4.30 | 4.57 | .70 |
| COL6 | 22 | 5.95 | 4.98 | 1.06 | ||
| LAMA2 | 20 | 2.48 | 3.31 | .74 | ||
| Myopinch | TOTAL | 40 | 1.89 | 1.83 | .29 | |
| COL6 | 21 | 2.55 | 2.06 | .44 | ||
| LAMA2 | 19 | .97 | 1.07 | .24 | ||
| Moviplate | TOTAL | 39 | 52 | 15 | .29 | |
| COL6 | 21 | 56.95 | 17.58 | 3.75 | ||
| LAMA2 | 18 | 38.56 | 17.75 | 3.96 |
MFM32 = Motor Function Measure; Distal-D3 = MFM Dimension 3; Jebsen = Jebsen Taylor Hand Function Test; QUEST = Quality of Upper Extremity Skills Test; Myometry = Hand Held Dynamometry-muscle strength; Goniometry = range of motion; Myoset Tools = upper extremity strength and function; Total = all participants; COL6 = collagen Vl-related muscular dystrophy; LAMA2 = laminin alpha 2-related dystrophy; N = number of participants; Mean of measures; SD = standard deviation; SE = standard error.