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. Author manuscript; available in PMC: 2018 Mar 1.
Published in final edited form as: Mol Genet Metab. 2016 Dec 8;120(3):198–206. doi: 10.1016/j.ymgme.2016.12.002

Table 2.

Relative abundance of CPS1, OTC and NAGS in liver.

Enzymatic activity (μmol/min/mg)
CPS1
NAGS OTC
WT M792I
Liver 4.8 × 10−2 [58] 0.9 × 10−3 [35] 1.2 × 10−3 [59] 0.7 [58]
Recombinant protein 1.31 [54] 0.04 14.6 [60] 30 [61]
Relative abundance 3.7 × 10−2 2.0 × 10−2 8.2 × 10−5 2.3 × 10−2