Table 2.
A summary of reported giant pheochromocytomas with maximal diameter greater than 10 cm, arranged by largest to smallest maximum diameter. The weight was not recorded in many of the papers.
| Author/year | Sex/age | Country | Size (cm)/weight (g) | Location | Presentation | Histopathological evaluation | Metastasis |
|---|---|---|---|---|---|---|---|
| Grissom et al./1979 [4] | F/54 | USA | 45 × 25/3000+ | Left abdomen | Asymptomatic | Unknown | None |
| Costa et al./2008 [5] | M/46 | Brazil | 30/unknown | Right adrenal | Abdominal pain | Malignant | Liver |
| Basso et al./1996 [6] | M/47 | Italy | 29 × 21 × 12/4050 | Left abdomen | Asymptomatic | Malignant | None |
| Karumanchery et al./2012 [7] | F/85 | England | 28 × 16 × 13/2300 | Left abdomen | Lower back pain | Unknown | None |
| Current case | F/50 | Trinidad & Tobago | 27 × 18 × 12/3315 | Left abdomen | Lower back pain | Low risk of malignancy | None |
| Gupta et al./2016 [8] | F/65 | India | 25 × 17 × 15/2750 | Left abdomen | Asymptomatic | Benign | None |
| Okuda et al./2013 [9] | F/43 | Japan | 24 × 23 × 16/5900 | Abdomen | Vulva edema | Unknown | None |
| Suga et al./2000 [10] | M/48 | Japan | 21 × 13 × 21/3900 | Left abdomen | Asymptomatic | Unknown | None |
| Terk et al./1993 [11] | M/35 | USA | 21 × 20 × 11/2870 | Organ of Zuckerkandl | Disproportionate abdominal girth, hypertension | Unknown | None |
| Soufi et al./2012 [12] | F/17 | India | 21 × 15 | Right upper abdomen | Asymptomatic | Malignant | None |
| Arcos et al./2009 [13] | F/36 | Canada | 21 × 17 × 11 | Left abdomen | Lower back pain | Malignant | Lymph node |
| Melegh et al./2002 [14] | M/55 | Hungary | 20/unknown | Left renal hilus | Asymptomatic | Unknown | None |
| Korgali et al./2014 [15] | M/63 | Turkey | 20 × 17 × 9/1736 | Left adrenal gland | Chest pain, sweating, nausea | Malignant | Rib |
| Ambati et al./2014 [16] | F/77 | Canada | 19 × 18 × 12/2460 | Right retroperitoneum | Dyspnea | Benign | None |
| Pan et al./2008 [17] | M/46 | USA | 18 × 14 × 13/1450 | Left abdomen | Episodic hypertension and headache | Unknown | Unknown |
| Uysal et al./2015 [18] | M/37 | Turkey | 18 × 8 × 13 | Left abdomen | Hypertension | Malignant | Multiorgan∗ |
| Sharma/2006 [19] | M/55 | India | 17 × 12/850 | Right adrenal gland | Asymptomatic | Benign | None |
| Daughtry et al./1977 [20] | M/53 | USA | 17/1150 | Unknown | Mild hypertension | Unknown | Unknown |
| Gupta et al./2016 [8] | M/40 | India | 16.4 × 14 /1836 | Left thyroid gland | Severe hypertension | Unknown | Unknown |
| Costa et al./2008 [5] | F/43 | Brazil | 16 | Right upper abdomen | Abdominal pain | Malignant | Unknown |
| Jain and Agarwal /2002 [21] | F/26 | India | 16 × 11 | Left abdomen | Asymptomatic | Malignant | Unknown |
| Wu et al./2000 [22] | F/49 | USA | 15 × 12 × 12 | Right upper abdomen | Asymptomatic | Unknown | Unknown |
| Santarone et al./2008 [23] | F/81 | Italy | 13 | Right upper abdomen | Hypertension, palpitation, sweating | Unknown | Unknown |
| Sundahl et al./2016 [24] | F/54 | Sweden | 12.5 × 10 × 3/204 | Right adrenal gland | Asymptomatic | Benign | None |
| Zhu et al./2014 [25] | F/67 | Japan | 12.1 × 10.8 | Left adrenal gland | Dizziness, vomiting, and stomachache | Unknown | None |
| Ikegami et al./2009 [26] | M/47 | Japan | 12 × 10 | Abdomen | Back pain | Unknown | Unknown |
| Li et al./2012 [27] | M/56 | Canada | 12 × 11 × 11 | Right upper abdomen | Progressive weight loss and nausea | Benign | None |
| Kakoki et al./2015 [28] | M/70 | Japan | 12 × 11 × 8/530 | Left adrenal gland | Ileus after hypertension medication | Benign | None |
| Schnakenburg et al./1976 [29] | M/12 | Ukraine | 12 × 10 × 9/1100 | Right abdomen | Hemihypertrophy | Malignant | Lung, brain |
| Filippou et al./2003 [30] | M/70 | Greece | 12 × 8 × 10 | Left abdomen | Asymptomatic | Malignant | None |
| Sarveswaran et al./2015 [31] | F/59 | India | 11.2 × 9.6 × 9.8 | Right suprarenal region | Upper right abdominal discomfort | Unknown | Unknown |
| Chan et al./2000 [32] | M/63 | China | 11 × 6.6 × 11 | Right suprarenal region | Asymptomatic | Malignant | Bone, lung |
| Awada et al./2003 [33] | F/26 | USA | 11 × 10 × 9 | Right adrenal gland | Dyspnea, paresthesia, chest pain, palpitation | Unknown | Unknown |
| Goldberg et al./2011 [34] | F/27 | Canada | 10.5 × 10.6 | Right adrenal gland region | Headaches, episodic palpitations, pallor | Unknown | Unknown |
| Antedomenico and Wascher/2005 [35] | F/39 | USA | 10.5/782 | Left upper abdomen | Abdominal pain | Unknown | Unknown |
| Wang et al./2015 [36] | F/36 | China | 10.3 × 9.3 | Left upper abdomen | Abdominal pain | Unknown | Unknown |
| Basiri and Radfar/2010 [37] | M/53 | Iran | Unknown/3150 | Left abdomen | Abdominal pain | Benign | None |
M, male; F, female. ∗Liver, lymph nodes, right adrenal gland, lungs, and bones.