Table 1. Patient demographics.
Adult | Pediatric | |||
---|---|---|---|---|
NF | IDC | NF | IDC | |
Sample size | 10 | 10 | 22 | 42 |
Sex | 50% M | 50% M | 54% M | 48% M |
Median Age At Tissue Collection (Years) |
42.5 (19–61) | 51 (20–60) | 12.7 (1.3–17) | 4.0 (0.05–17.7) |
Mean EF ± SD (%) | 56.4 ± 10.8 | 14.0 ± 5.2 | 48.3 ± 15.2 | 25.4 ± 6.0 |
Inotropes | 7 (70%) | 2 (20%) | - | 32 (76%) |
Digoxin | - | 2 (20%) | - | 15 (35%) |
ACEI | - | 2 (20%) | - | 31 (74%) |
Beta-Blocker | - | 3 (30%) | - | 8 (19%) |
Presence of Fibrosis | NA | NA | NA | 21 (50%) |
Type of Fibrosis | NA | NA | NA | 17 (81%) Endocardial; 2 (9.5%) Interstitial; 2 (9.5%) Both |