(A) Yemeni Jewish family with extreme hypotonia, severe arthrogryposis, and respiratory failure in 2 of 7 children. Genotypes of SLC18A3 c.1078 G>C, p.Gly360Arg are indicated below each sampled individual. (B) X-ray of III-3 at age 4 days illustrates the endotracheal tube, widespread opacities in both lungs, and arthrogryposis. (C) Sequences of SLC18A3 c.1078 G>C in genomic DNA of an unrelated control with wild-type (WT) sequence, and of family members who are heterozygous (HET) and homozygous (HOM) for the mutation. The 2 youngest sisters were not available for analysis. Nucleotides and expected amino acid sequence are shown above the chromatograms.