Table 1.

Patient’s characteristics

Subject	Age at time of CMR (y)	Gender	BSA (m2)	Ventricular morphology	Type of Fontan	Diagnosis	APC	Complications	NYHA
1	3	M	0.56	Left	Extracardiac	Unbalanced AVSD, small LV, PA, MAPCA, right isomerism, bilateral SVC, dextrocardia. Fenestrated*	*	PLE	NYHA II
2	7	M	0.82	Left	Extracardiac	HLHS	Yes	Restrictive ASD	NYHA III
3	4	M	0.68	Right	Extracardiac	HLHS, TAPVD, bilateral SVC	Yes	PLE	NYHA IV
4	12	F	1.26	Right	Extracardiac	Hypoplastic right PA, left isomerism, interrupted IVC, dextrocardia	No	Pulmonary arteriovenous fistulas	NYHA IV
5	4	M	0.72	Right	Extracardiac	Hypoplastic aortic arch, CoA, VSD, DORV	Yes	LPA stenosis	NYHA II
6	15	M	1.60	Right	Extracardiac	DORV Taussig Bing, unbalanced AVSD, PS, TAPVD, right isomerism	Yes	APC	NYHA II
7	17	M	1.72	Right	Lateral tunnel	Single ventricle, DORV, TGA, dextrocardia	No	No	NYHA I
8	14	F	1.37	Right	Extracardiac	Single ventricle, PS, TGA, right isomerism, bilateral SVC, TAPVD	Yes	No	NYHA I
9	13	F	1.36	Left	Extracardiac	TGA, multiple VSD, hypoplastic pulm arteries	Yes	No	NYHA I
10	29	M	1.72	Left	Right atrium to PA	Tricuspid atresia	No	No	NYHA I
11	4	M	0.72	Left with long outflow tract	Extracardiac	DILV, TGA, PS, left pulm artery stenosis	No	No	NYHA II

CMR cardiac magnetic resonance; BSA body surface area; APC aortopulmonary collaterals; NYHA New York Heart Association Functional Classification; AVSD atrioventricular septal defect; LV left ventricle; MAPCA major aortopulmonary collateral arteries; SVC superior vena cava; HLHS hypoplastic left heart syndrome; TAPVD total anomalous pulmonary venous drainage; IVC inferior vena cava; CoA coarctation of aorta; VSD ventricular septal defect; DORV double outlet right ventricle; PS pulmonary stenosis; TGA transposition of the great arteries; DILV double inlet left ventricle; PLE protein-losing enteropathy; ASD atrial septal defect; LPA left pulmonary artery

*Fenestrated extracardiac tunnel which makes the assessment of APC difficult