TABLE I.
Participant | Age (years) | Hearing history | Etiology | Age at 1st activation (years) | Age at 2nd activation (years) | Internal device (L, R) | Base pair (L, R) | Middle pair (L, R) | Apical pair (L, R) | Base prop. DR (L, R) | Middle prop. DR (L, R) | Apex prop. DR (L, R) |
---|---|---|---|---|---|---|---|---|---|---|---|---|
CIDX | 11.6 | Pro.a HLb ID at birth | Connexin 26 | 1.43 | 2.59 | CI24R(CS), CI24R(CS) | 4, 4 | 12, 12 | 20, 18 | 0.87, 0.87 | 0.77, 0.89 | 0.88, 0.88 |
CIDQ | 12.2 | ID at birth | Connexin 26 | .82 | 4.34 | CI24RE, CI24R(CS) | 4, 4 | 12, 12 | 20, 20 | 0.77, 0.60 | 0.76, 0.66 | 0.72, 0.66 |
CIDJ | 13.1 | ID at 12 months | Hereditary | 1.62 | 5.04 | CI24RE, CI24R(CS) | 6, 6 | 12, 12 | 20, 18 | 0.75, 0.86 | 0.77, 0.84 | 0.73, 0.85 |
CIEV | 13.2 | Progressed from sev.c to pro. by 2–3 years | Hereditary | 2.67 | 10.95 | CI24RE, CI24R(CA) | 4, 6 | 12, 14 | 20, 20 | 0.83, 1 | 0.80, 1 | 0.79, 0.94 |
CIAG | 13.3 | Progressed from mod.d–sev. (L) and sev.-pro. (R) to pro. by 15 months | Connexin 26 | 1.72 | 3.12 | CI24R(CS), CI24R(CS) | 4, 4 | 12, 12 | 20, 20 | 0.68, 0.76 | 0.74, 0.71 | 0.81, 0.63 |
CIAW | 13.6 | Pro. HL ID at 3 months | Congenital CMV | 1.21 | 5.46 | CI24RE, CI24R(CS) | 4, 4 | 12, 8 | 20, 22 | 0.5, 0.82 | 0.66, 0.73 | 0.58, 0.81 |
CIBO | 14.2 | Progressed from mod. to pro. HL by 28 months | EVAS/ Pendred syndrome | 2.83 | 3.90 | CI24R(CS), CI24R(CS) | 4, 4 | 12, 12 | 20, 18 | 0.93, 0.97 | 0.92, 1 | 0.93, 1 |
CIAP | 14.7 | Progressed from mild to sev.-pro. by 3 years | Unknown | 3.47 | 5.10 | CI24R(CA),CI24R(CA) | 4, 4 | 12, 10 | 20, 16 | 1, 1 | 1, 0.95 | 1, 1 |
CIBK | 15.2 | ID at 17 months | Connexin 26 | 2.14 | 7.11 | CI24RE, CI24R(CS) | 4, 4 | 12, 12 | 20, 18 | 0.76, 0.82 | 0.71, 0.85 | 0.72, 0.84 |
CIEU | 16.2 | Progressed from sev. to pro. by age 4 (R) and 8 (L) years | Hereditary | 4.28 | 10.45 | CI24RE, CI24R(CS) | 4, 4 | 12, 12 | 18, 18 | 0.75, 0.73 | 0.63, 0.78 | 0.65, 0.84 |
CIAQ | 17.5 | Pro. HL ID at 13 months | Connexin 26 | 4.00 | 8.21 | CI24R, CI24R | 4, 4 | 12, 13 | 20, 19 | 0.89, 0.9 | 0.88, 0.91 | 0.89, 0.89 |
Profound.
Hearing loss.
Severe.
Moderate.