Table 1.
Estimating the incidence of ARPKD using Cerner Health Facts® Data.
| HF ARPKD patients (<1 month) | HF (<1 month) | ARPKD incidence in HFa | NVS | HF/NVS (%) | ARPKD annual new patientsb | Adjusted ARPKD annual new patientsc | |
|---|---|---|---|---|---|---|---|
| 2010 | 9 | 279,902 | 1:31,100 | 3,999,386 | 7.00 | 129 | 102 |
| 2011 | 13 | 322,416 | 1:24,801 | 3,953,590 | 8.16 | 159 | 126 |
| 2012 | 9 | 297,885 | 1:33,098 | 3,952,841 | 7.54 | 119 | 94 |
| 2013 | 11 | 295,432 | 1:26,857 | 3,932,181 | 7.51 | 146 | 115 |
| 2014 | 15 | 313,988 | 1:20,933 | 3,988,076 | 7.87 | 191 | 151 |
| AVG | 11 | 301,925 | 1:26,485 | 3,965,215 | 7.61 | 150 | 118 |
aHF ARPKD < 1 month/HF < 1 month.
bHF ARPKD < 1 month/HF/NVS.
cBased on 79% ARPKD neonatal survivor rate in HF data set.
ARPKD, autosomal recessive polycystic kidney disease; HF, Health Facts® Dataset (using discharge data); NVS, National Vital Statistics data.