Table 2. Clinical characteristics and laboratory variables of CNL patients.
| No. | Age | Sex | Diagnosis | WBC | N% | HB | BPC | PB Blast |
BM Blast |
Karyotypes | CSF3R | SETBP1 | SRSF2 | Disease progression | Death |
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
| 1 | 33 | M | CNL | 21.6 | 94.1 | 153 | 115 | 0 | 1.2 | NK | T618I/ W818X |
WT | WT | N | N |
| 2 | 65 | M | CNL | 26.9 | 86.0 | 76 | 17 | 0 | 3.6 | NK | T618I/ Q749X |
D874N | WT | N | N |
| 3 | 27 | F | CNL | 62.5 | 80.3 | 72 | 17 | 10 | 6.4 | NK | T618I | WT | WT | Y | Y |
| 4 | 56 | M | CNL | 134.5 | 96.1 | 118 | 20 | 7 | 8.4 | NK | T618I | WT | WT | N | N |
| 5 | 34 | M | CNL | 26.5 | 81.2 | 74 | 224 | 0 | 3.6 | 47,XY, +8 |
T618I | WT | WT | N | N |
| 6 | 32 | M | CNL | 28.0 | 86.8 | 63 | 188 | 0 | 3.6 | NK | T618I | WT | WT | N | N |
| 7 | 44 | M | CNL | 39.7 | 88.6 | 129 | 273 | 0 | 1.6 | NK | T618I | WT | WT | N | Y |
| 8 | 92 | M | CNL | 20.6 | 88.5 | 117 | 331 | 0 | 0.0 | NK | P733T | WT | WT | N | N |
| 9 | 57 | M | CNL | 84.8 | 96.1 | 81 | 50 | 0 | 1.6 | NK | WT | WT | WT | N | N |
| 10 | 77 | M | MGUS- CNL |
55.2 | 90.2 | 129 | 227 | 0 | 0.0 | NK | WT | WT | WT | Y | Y |
CNL, Chronic neutrophilic leukemia; MGUS-CNL, undetermined significance monoclonal gammopathy associated with chronic neutrophilic leukemia; WBC, white blood cell; N%, neutrophil percentage; HB, hemoglobin; BPC, blood platelet cell; PB Blast, blast cell count of peripheral blood; BM Blast, blast cell count of bone marrow; NK, abnormal karyotype; WT, wild type; CSF3R, colony-stimulating factor 3 receptor;SETBP1, SET-binding protein 1; SRSF2, serine/arginine-rich splicing factor 2.