Table 2.
International Criteria for Behçet’s disease – point score system: scoring ⩾4 indicates Behçet’s disease.
| Sign/symptom | Score |
|---|---|
| Oral aphthosis | 2 |
| Genital aphthosis | 2 |
| Ocular manifestations | 2 |
| Skin manifestations | 1 |
| Vascular manifestations | 1 |
| Central nervous system involvement | 1 |
| Positive pathergy testa | 1 |
Source: Reproduced from International Team for the Revision of the International Criteria for Behçet’s Disease (ITR-ICBD) 2014, with permission.
a
Pathergy testing optional; where conducted, 1 extra point may be assigned for a positive result (a positive pathergy test indicates that the immune system is overreacting to a minor injury).