Table 1.
CF patient demographics
| CF | Sex | Age | CFTR genotype | FEV 1 | BMI | PI | Ps . | Sa . | Asp. |
|---|---|---|---|---|---|---|---|---|---|
| 1 | M | 21 | ΔF508/R506T > K | 17% | 30.5 | Y | + | + | − |
| 2 | M | 29 | ΔF508/ΔF508 | 64% | 20.24 | Y | + | − | − |
| 3 | F | 25 | ΔF508/R177H 5T | 89% | 23.15 | N | - | + | = |
| 4 | M | 18 | ΔF508/ΔF508 | 87% | 20.89 | Y | + | + | + |
| 5 | M | 23 | ΔF508/unknown | 27% | 17.76 | Y | + | - | - |
| 6 | F | 19 | ΔF508/ΔF508 | 54% | 21.71 | Y | + | - | - |
| 7 | F | 25 | ΔF508/1717GA | 51% | 19.62 | Y | + | - | + |
| 8 | M | 31 | ΔF508/621 + 1G → T | 83% | 22.77 | Y | + | - | + |
FEV1, forced expiratory volume in 1 s percent predicted; BMI, body mass index; PI, pancreatic insufficiency (Y, yes; N, no); Ps., colonisation with Pseudomonas aeruginosa; Sa., colonisation with Staphylococcus aureus; Asp., colonisation with Aspergillus species.