Table 2.
Family‐specific clinical characteristics
| Family | Number F/M | Mean age (years) | Symptom onset | Prophylaxis yes/no | Number of attacks without prophylaxis |
|---|---|---|---|---|---|
| A |
40 18/22 |
46 s.d. 20 |
8 s.d. 5 |
19/21 |
Frequent: 3 Intermediate: 6 Rare: 9 Very rare: 3 |
| B |
7 5/2 |
35 s.d. 14 |
11 s.d. 7 |
1/6 |
Frequent: 0 Intermediate: 1 Rare: 3 Very rare: 2 |
| C |
8 4/4 |
37 s.d. 19.8 |
9 s.d. 3.6 |
2/6 |
Frequent: 0 Intermediate: 2 Rare: 3 Very rare: 1 |
| D |
9 6/3 |
55 s.d. 16.5 |
14 s.d. 8.2 |
2/7 |
Frequent: 0 Intermediate 3 Rare: 1 Very rare: 3 |
| E |
1 1/0 |
25 | 2 | 1/0 | – |
| F |
1 1/0 |
47 | 9 | 0/1 | Frequent:1 |
| G |
1 1/0 |
43 | 5 | 1/0 | – |
| H |
2 1/1 |
50 s.d. 24 |
27 s.d. 8 |
0/2 |
Frequent: 1 Rare: 1 |
| I |
1 1/0 |
45 | 27 | 0/1 | Intermediate:1 |
F = female; M = male; s.d. = standard deviation. Frequent number of attacks: ≥ 1/week. Intermediate number of attacks: ≤ 1/week; ≥ 1/month. Rare number of attacks: ≤ 1/month; ≥ 1/year. Very rare number of attacks: < 1/year.