This is a 29-year-old white male with a clinical history of Leukemia, dizziness, and left severe sensorineural hearing loss. His hearing loss was fluctuant. Histopathologic evaluation of the ear showed: hypertrophied middle ear mucosa, fibrous tissues in the posterior side of the middle ear, profound endolymphatic hydrops (arrows), severe loss of haircells, and strial atrophy (open arrow head).