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. 2017 Apr 24;10:1179545x17705863. doi: 10.1177/1179545x17705863

Table 1.

WHO classification of mature T and NK neoplasms.4

Usually indolent
T-cell large granular lymphocytic leukemia
Hydroa vacciniforme-like lymphoproliferative disorder
Indolent T-cell lymphoproliferative disorder of the gastrointestinal tract
Subcutaneous panniculitis-like T-cell lymphoma
Mycosis fungoides
Primary cutaneous CD30-positive T-cell lymphoproliferative disorders
Lymphomatoid papulosis
Primary cutaneous anaplastic large cell lymphoma
Primary cutaneous acral CD8-positive T-cell lymphoma
Primary cutaneous CD4-positive small/medium T-cell lymphoproliferative disorder
Breast implant–associated anaplastic large cell lymphoma
Usually aggressive
Nodal Extranodal
Systemic EBV-positive T-cell lymphoma of childhood Extranodal NK/T-cell lymphoma, nasal type
Adult T-cell leukemia/lymphoma Enteropathy-associated T-cell lymphoma
Peripheral T-cell lymphoma, not otherwise specified Monomorphic epitheliotropic intestinal T-cell lymphoma
Angioimmunoblastic T-cell lymphoma Hepatosplenic T-cell lymphoma
Follicular T-cell lymphoma Sézary syndrome
Nodal peripheral T-cell lymphoma with TFH phenotype Primary cutaneous gamma-delta T-cell lymphoma
Anaplastic large cell lymphoma
Anaplastic lymphoma kinase positive
Anaplastic lymphoma kinase negative
Primary cutaneous CD 8–positive aggressive epidermotropic cytotoxic T-cell lymphoma
Typically leukemic presentation
T-cell prolymphocytic leukemia
Chronic lymphoproliferative disorder of NK cells
Aggressive NK-cell leukemia

Abbreviations: EBV, Epstein-Barr virus; NK, natural killer; TFH, follicular helper T; WHO, World Health Organization.