Table 3.
Pulmonary function testing before and after 7 and 24 weeks of therapy
| Initial | Week 7 | Week 24 | |
|---|---|---|---|
| FVC, liters | 2.42 (1.34–3.55)a | 2.30 (1.08–3.87) | 2.41 (1.15–3.65) |
| Change in FVC from Week 0 | −0.08 (−0.31, +0.40) | −0.05 (−0.28, +0.19) | |
| FVC % predicted | 66 (41–83) | 69 (39–86) | 69 (40–91) |
| Change in FVC % predicted from week 0, % | −2.4 (−9.0, 11.0) | −2.0 (−9.0,+16.0) | |
| FEV-1, L | 1.63 (0.83–2.3) | 1.58 (0.74–2.69) | 1.55 (0.69–2.35) |
| Change in FEV-1 from week 0, L | −0.02 (−0.21, +0.41) | −0.12 (−0.48, +0.13) | |
| FEV-1% predicted | 46 (36–79) | 48 (30–94) | 46 (24–95) |
| Change in FEV-1% predicted from week 0, % | −0.5 (−10.0, +15) | −3.0 (−17, +16.0) | |
| FEV-1/FVC | 70 (48–90) | 68 (47–87) | 62 (41–86) |
| Change in FEV-1/FVC from week 0, % | 0.01 (−0.04, +0.07) | −0.02 (−0.31, +0.04) | |
| DLCO mm Hg | 14 (7.8–22.88) | 15.54 (7.7–23.38) | 15.28 (5.8–24.14) |
| Change in DLCO from week 0 | 0.64 (−5.01, +6.28) | ||
| DLCO % predicted | 59 (23–81) | 58 (33–84) | 62 (24–99)b |
| Change in DLCO % predicted from week 0, % | 9.5 (−14.0, +27) | ||
| 6MWD, m | 381 (152–610) | 408 (183–655) | 388 (152–701) |
| Change in 6MWD, m | 0 (−69 to 175) | 0 (−137 to 297) |
aMedian (range)
bDiffers from week 0, p = 0.0419