Table 3. Clinical Characteristics of Children Inactivated from Transplant List.

Five children were listed, but later inactivated due to improved or stable lung function. Clinical data for 4 of the 5 children are presented here. LPM: liters per minute of oxygen

Genetic Etiology	Age of symptom onset (months)	Age at listing (months)	Maximum respiratory support	Respiratory support at time of listing	Respiratory support at time of inactivation	Reason for inactivation	Medications	Respiratory support and age at last follow up
SFTPC c.218T>C p.I73T	14	24	Invasive endotracheal mechanical ventilation	4 LPM	3 LPM	Stable lung function	Pulse solumedrol, hydroxychloroquine, furosemide, albuterol	3 LPM; 7.5 years
SFTPC c.325-1 G>A	4	72	2 LPM	2 LPM	1–2 LPM	Stable lung function	Prednisone, furosemide, albuterol	1 LPM; 11.5 years
SFTPC c.565T>G p.C189G	0.5	24	Invasive endotracheal mechanical ventilation	0.5 LPM	Room air	Improved lung function	Pulse solumedrol, prednisone, cyclosporine, IVIG	Room air; 13 years
ABCA3 c.3609_3611delCTT (p.F1203del)/c.4751delT (p.L1584Rfs*50)	16	18	15 LPM	3 LPM	3 LPM	Stable lung function	Prednisone, hydroxychloroquine, azithromycin	3 LPM; 9 years