Table 1.

Selected studies describing portal hypertension and esophageal varices in autosomal recessive polycystic kidney disease.

	Study type	n	Definition of portal hypertension	Portal hypertension	Underwent endoscopy	Varices on endoscopy	Number of patients with variceal bleed
Capisonda et al.	Retrospective	27	Patent portal vein, hepatofugal portal flow, splenomegaly, and the presence of varices	10/27 (37%)	Unknown	Unknown	3/27 (11%)
Gunay-Aygum et al.	Prospective	72	Spleen length/height ratio	47/72 (65%)	31/72 (43%)	24/31 (77%)	4/72 (5%)
Luoto et al.	Retrospective	27	Splenomegaly plus thrombocytopenia (platelet count <150) OR esophageal varices	13/27 (48%)	16/27 (59%)	8/27 (30%)	4/27 (15%)
Srinath et al.	Systematic Review	788	Splenomegaly, esophageal varices, or hypersplenism	286/639 (45%)	Unknown	92/315 (29%)	38/315 (12%)