Fig. 2.

The proportion of Aβ positivity and topographical distribution of Aβ in frontotemporal dementia (FTD) syndromes with and without motor impairment. The proportion of patients that demonstrate no Aβ deposition (A0), Aβ in the frontal-temporal cortices (A1), additional Aβ in the basal ganglia (A2), and additional Aβ in the substantia nigra (A3) is shown in patients with behavioral variant FTD cases without motor impairment (bvFTD), primary progressive aphasia cases without motor impairment (PPA), cases with motor neuron disease (MND), and cases with extrapyramidalism. As only one PPA case without motor impairment had an A3 distribution (4%, 1/26), this has been combined with the A2 group.