Table 1.
Individual baseline characteristics.
| Gender | Age | Extrapulmonary disease | Pack | VEGF-D | ||||
|---|---|---|---|---|---|---|---|---|
| Patient | (M/F) | (years) | Disease | manifestation(s) | Positive gene test | Type of biopsy | years | (pg ml–1) |
| 1 | F | 34 | Unclass. | – | – | – | 18 | 471 |
| 2 | F | 44 | PLCH | – | – | VATS | 26 | – |
| 3 | M | 49 | BHDS | Renal cysts | + | – | – | – |
| 4 | F | 38 | LAM | TS, skin lipoma, angiomyolipoma | + | – | – | 846 |
| 5 | F | 76 | LAM | – | – | – | – | – |
| 6 | F | 61 | PLCH | – | – | fTBB | 43 | – |
| 7 | M | 46 | BHDS | Renal cysts | + | – | – | – |
| 8 | F | 64 | LAM | – | – | VATS | – | > 4000 |
| 9 | F | 36 | LAM | – | – | Abdominal biopsy | 5 | > 4000 |
| 10 | F | 39 | LAM | – | – | VATS | – | 2512 |
| 11 | F | 71 | LAM | TS (genotype), angiomyolipoma | + | – | – | 2310 |
| 12 | M | 26 | PLCH | – | – | VATS | 12 | – |
Abbreviations: – = none/not performed. M = male. F = female. LAM = lymphangioleiomyomatosis. PLCH = pulmonary Langerhans cell histiocytosis. BHDS = Birt-Hogg-Dubé syndrome. Unclass. = unclassified cystic lung disease. fTBB = forceps transbronchial biopsy. VATS = video-assisted thoracoscopic surgery. VEGF-D = vascular endothelial growth factor D. pg ml–1 = pictogram per millilitre.