Table 2. Clinical and biochemical characteristics of the patient before and after treatment with carnitine (200 mg/kg per day).

	Plasma-free carnitine levels (μmol/l)	Plasma total carnitine level (μmol/l)	Hemoglobin level (g/dl)	LVPWd (mm)	IVSd (mm)
Reference	30–50	43–65	11–13	3.59–7.31	4.38–8.00
Before treatment	0	<1	7	8.3 (z-score 3.26)	10.5 (z-score 3.45)
After 3 months of the treatment	5	8	14	6.8 (z-score 1.98)	7.9 (z-score 1.95)
After 12 months of the treatment	5	8	12	5.8 (z-score 1.07)	6.0 (z-score 0.94)

Abbreviations: IVSd, end-diastolic interventricular septal thickness; LVPWd, end-diastolic left ventricular posterior wall thickness.

Z-scores were calculated from reference.¹¹