Table 3.
Michaelis-Menten kinetics as determined by 4MU substrates.
4MU-α-GAL |
4MU-α- NAGAL |
|||||||
---|---|---|---|---|---|---|---|---|
Km (mM) | Vmax (mmol/h/mg) | kcat (s-1) | kcat/Km (mM/s-1) | Km (mM) | Vmax (mmol/h/mg) | kcat (s-1) | kcat/Km (mM/s-1) | |
α-GAL | 2.478 | 4.219 | 55.96 | 22.58 | No activity detected | |||
α-NAGAL | 6.02 | 0.527 | 6.89 | 1.14 | 0.7 | 3.9 | 25.51 | 36.13 |
α-NAGALEL | 3.18 | 0.71 | 14.52 | 4.79 | No activity detected | |||
Fabrazyme | 2.431 | 3.954 | 52.11 | 21.43 | No activity detected |