Figure 1.
In Vitro Uptake of BMN 250 in Normal Mouse Hippocampal Neurons
(A) Representative confocal images of cultured mouse hippocampal neurons treated with Alexa Fluor 488-labeled BMN 250 (green) and LysoTracker red (red), showing localization of NAGLU signals to lysosomes (yellow), with arrows indicating representative co-localized signals. (B) IGF2/mannose 6-phosphate receptor-dependent uptake of BMN 250 by normal mouse neurons was significantly inhibited by IGF2. NAGLU activity in cell lysates, expressed as the fold elevation (mean ± SD, n = 3) above normal levels. ***p < 0.001.