Table 2.
Demographic descriptions of the 36 subjects with genetically confirmed CFLD.
| Feature | All Subjects | Data by New CFLD Criteria | ||
|---|---|---|---|---|
| CFLD | No CFLD | p-value | ||
| Number of Patients | 36 | 17 | 19 | |
| Male/Female | 26/10 | 15/2 | 11/8 | 0.06 |
| Caucasian/Other | 35/1 | 16/1 | 19/0 | |
| Alive/Dead at end of follow-up | 25/11 | 13/4 | 12/7 | |
| Median age of CF diagnosis (IQR) | 11.0 (2.6, 21.7) | 5.2 | 11 | 0.57 |
| Median age at time of enrollment (IQR) | 20.1 (15.3, 29.8) | 16.8 | 26.8 | 0.15 |
| Median duration of follow-up (IQR) | 24.5 (15.6, 32.9) | 28 | 21.5 | 0.08 |
| Genotype | ||||
| ΔF508/ΔF508 | 12 | 8 | 4 | 0.67 |
| ΔF508/Other | 9 | 5 | 4 | 0.29 |
| Other | 6 | 0 | 6 | 0.01 |
| Unknown | 9 | 4 | 5 | 0.43 |