Figure 2.
Structural imaging of Case 3. Montage color fundus photos of the right (A) and left (B) eyes show vascular attenuation, perivascular and peripheral retinal pigment epithelium atrophy, and pigment clumping. Fundus autofluorescence of the right (C) and left eyes (D) show perivascular and peripheral hypoautofluorescence and peripapillary and macular hyperautofluorescence. Spectral-domain optical coherence tomography of the right (E) and left (F) eyes show segmental outer retinal disruption (arrows), with relative foveal sparing, epiretinal membranes in both eyes, and cystoid macular edema in the left eye.