Table 2.
Reported cases of composite pheochromocytoma/paragangliomas associated with MEN 2A/B
| Age(years)/sex | MEN type | Tumor size/weight | Organ | Neurogenic component | Outcome | Reference/country/year |
|---|---|---|---|---|---|---|
| 34/M | 2A | 1.6 cm/11,8g | Left adrenal medulla | Ganglioneuroma | Uneventful postoperative course | Brady et al. [6]/USA/1997 |
| 49/M | 2A | 600g | Left adrenal medulla | Ganglioneuroblastoma | Died after orthopedic surgery (postmortem incidental finding) | Matias-Guiu et al. [7]/Spain/1998 |
| 27/F | 2B | 10 cm/124g | Left adrenal medulla | Ganglioneuroma | Tumor free for 16 months after surgery | Charfi et al. [8]/Tunisia/2008 |
| 59/M | 2B | 3 cm | Retroperitoneum | Ganglioneuroma | Metastatic disease at diagnosis | Yamasaki et al. [9]/Japan/2016 |
| 40/F | 2A | 9 cm | Right adrenal medulla | Ganglioneuroma | Tumor free for 3 years | Our case/Morocco |
MEN2A/2B multiple endocrine neoplasia type 2A or 2B, M Male, F Female