Table 2.

Kid-Short Marfan Score (Kid-SMS) [8].

Required Manifestations	Risk Category for Likelihood of MFS
SV + EL	Very high risk (Diagnosis of MFS according Ghent-2)
SV + MVP + TVP SV + PA SV + 3 Skeletal Features	High risk (Patient is at high risk of MFS. Complete examination of all symptoms of the revised Ghent Criteria is strictly recommended as soon as possible. Patient should see MFS specialists)
EL + MVP + TVP EL + PA
Family history SV	Moderate risk (Patient needs to be verified or excluded with further diagnostic procedures other than or echocardiography and clinical examination)

SV, dilatation of sinus of valsalvae; EL, ectopia lentis; MVP, mitral valve prolapse; TVP, tricuspid valve prolapse; PA, dilatation of pulmonary artery; 3 skeletal features, at least 3 skeletal features of the systemic score of the revised Ghent Criteria; Ghent-2, revised Ghent Criteria; MFS, Marfan syndrome.