Table 1.

Craniofacial and oral features associated with RRS and DRS (N/A: Not available, DRS: Dominant Robinow Syndrome, RRS: Recessive Robinow Syndrome).

	Mazzeu et al.(6)		Beiraghi et al.(4)		Present case
	DRS(%)	RRS(%)	DRS(%)	RRS(%)	RRS
CRANIOFACIAL FINDINGS
Frontal bossing	79	78	33	67	+
Orbital hypertelorism	44	100	78	100	+
Midface hypoplasia	81	94	33	67	+
Depressed nasal bridge	78	49	44	100	+
Wide nasal bridge	97	95	89	100	+
Short nose	81	93	100	100	+
Upturned nose	87	97	78	100	+
Anteverted nares	100	96	89	100	+
Triangular mouth	65	86	44	100	+
Down-slanted mouth corners	63	95	44	100	+
Micrognathia	57	68	22	0	-
Retrognathia	96	37	33	33	-
ORAL FINDINGS
Bifid tongue	39	59	67	67	Fissured tongue
Gingival hyperplasia	36	71	78	67	+
Dental malocclusion	49	94	0	67	+
Abnormal uvula	N/A	N/A	89	67	+
Wide retromolar ridge	N/A	N/A	100	33	-
Dental crowding	N/A	N/A	78	33	-
Flat palate	N/A	N/A	67	100	+
Short palate	N/A	N/A	67	67	-
Delay of dental eruption	N/A	N/A	56	67	+
Highly arched palated	51.5	14	0	0	+
Cleft lip/palate	35	13.5	56	0	-
Microdontia	N/A	N/A	0	0	-
Supernumerary teeth	N/A	N/A	89	0	-