Table 2.
Main characteristics and outcomes of the patients.
| Patients (N) |
Sex Age |
Symptoms duration (months) |
Symptoms | Date of diagnoses |
Histologic type (differentiation)/grading |
Site(s) of disease | IP (PAPS) mmHg |
Treatment after surgery | Time from surgery to CT (days) | N cycles of CT | Disease status | Overall survival (months) |
|---|---|---|---|---|---|---|---|---|---|---|---|---|
| 1 | F 45 |
9 | Dyspnea Right cardiac failure |
2010 | IS (fibrosarcoma) G2 |
Local M+ (lung, kidney, nodes) |
85 | CT∗ | 10 months∗ |
NA | PD | 26† |
| 2 | F 65 |
2 | Pain Cough |
2011 | IS (osteocondroid diff) G2 |
Local (bilateral) |
45 | CT | 50 | 6 | NED | 55 |
| 3 | M 32 |
9 | Fever Pain Dyspnea |
2012 | IS (undiff) G3 |
Local (unilateral) |
65 | CT | 22 | 6 | PD | 6† |
| 4 | F 74 |
8 | Dyspnea Pain |
2012 | IS (fibrous histiocytoma diff) G3 |
Local (unilateral) |
— | CT | 48 | 6 | PD | 8† |
| 5 | F 77 |
7 | Dyspnea Pain Cough Hemoptysis |
2012 | IS (mixofibrous diff) G2 |
Local M+ (lung) |
>60 | CT | 69 | 2 | PD | 6† |
| 6 | F 49 |
33 | Dyspnea | 2013 | IS (leiomuscolar diff) G2 |
Local M+ (lung) |
90 | CT | 42 | 5 | NED | 28 |
| 7 | F 64 |
15 | Dyspnea Pain Dysesthesia |
2014 | IS (undiff) G3 |
Local (bilateral) |
45 | CT/RT | 30 | 4 | NED | 21 |
| 8 | M 77 |
2 | Dyspnea Pain |
2015 | IS (undiff) G3 |
Local (bilateral) |
100 | CT/RT | 25 | 4 | PR | 11 |
| 9 | F 49 |
2 | Heart failure | 2015 | IS (undiff) G3 |
Local (bilateral) |
45 | CT/RT | 36 | 4 | NED | 10 |
| 10 | M 84 |
4 | Dyspnea Pain |
2015 | IS (undiff) G2 |
Local (bilateral) |
70 | CT | 44 | 4 | PD | 8 |
| 11 | F 37 |
6 | Dyspnea Hemoptysis |
2016 | IS (osteosarcoma diff) G3 |
Local (bilateral) |
— | CT | 30 | 4 | NED | 4 |
IS: intimal sarcoma; M+: metastatic disease; CT: chemotherapy (adriamycin and ifosfamide); RT: radiotherapy; NA: not applicable; PD: progressive disease; NED: not evidence of disease; PR: partial response. †Patient died. ∗CT was given at disease progression. The patient who died perioperatively was excluded.