Table 1.
SCA neuropsychology and demographic information
| Participant | Sex | Age, yr | Ed, yr | Handedness | Type | Diag, yr | Ataxia Scale | MoCA |
|---|---|---|---|---|---|---|---|---|
| Abrupt | ||||||||
| ARSCA1 | Female | 63 | 16 | Left | SCA8 | 11 | 27 | |
| ARSCA2 | Male | 73 | 20 | Left | SAOA | 4 | 20.5 | 28 |
| ARSCA3 | Male | 41 | 16 | Left | SAOA | 19 | 27 | 29 |
| ARSCA4 | Female | 55 | 14 | Right | SCA2 | 13 | 48 | 26 |
| ARSCA5 | Male | 47 | 16 | Left | SAOA | 19 | 22 | 29 |
| ARSCA6 | Male | 42 | 16 | Right | SCA2 | 2 | 41 | 28 |
| ARSCA7 | Male | 62 | 19 | Right | SAOA/MSA | 4 | 12 | 30 |
| ARSCA8 | Male | 70 | 16 | Right | SAOA/family hist | 9 | 11 | 27.5 |
| ARSCA9 | Male | 44 | 22 | Left | SAOA/MSA | 2 | 12 | 30 |
| ARSCA10 | Male | 40 | 16 | Right | SCA2 | 11 | 45 | 26 |
| Gradual | ||||||||
| GRSCA1 | Female | 35 | 17 | Right | SCA1 | 4 | 6* | 24 |
| GRSCA2 | Female | 30 | 17 | Left | SCA2 | 3 | 17* | |
| GRSCA3 | Male | 44 | 17 | Right | SCA1 | 1 | 9* | 19 |
| GRSCA4 | Male | 79 | 13 | Right | SAOA | 6 | 11* | 14 |
| GRSCA5 | Male | 46 | 17 | Right | ADCA | 1 | 7* | 20 |
| GRSCA6 | Male | 41 | 17 | Right | SAOA | 23.5* | 23 | |
| GRSCA7 | Male | 49 | 17 | Right | SAOA | 3 | 8* | 22 |
| GRSCA8 | Male | 36 | 17 | Right | SCA1 | 3 | 10.5* | 25 |
| GRSCA9 | Female | 69 | 19 | Left | SAOA | 8 | 3* | 30 |
| GRSCA10 | Female | 52 | 22 | Right | SCA6 | 14 | 1 | 28 |
Ed, education; Diag, years since diagnosis; SAOA, sporadic adult-onset ataxia; MSA, multiple system atrophy; ADCA, autosomal dominant cerebellar ataxia.
*
SARA; otherwise ICARS.