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. 2017 Aug;6(3):163–171. doi: 10.5582/irdr.2017.01044

Table 1. Classification of pulmonary hypertension based on etiology (9).

Group 1
  • Idiopathic

  • Heritable

  • Drug induced

  • Associated with conditions like connective tissue disease, HIV, congenital heart disease, schistosomiasis or chronic hemolytic anemia

  • Pulmonary veno occlusive disease (PVOD) and pulmonary capillary hemangiomatosis

 
Group 2
  • Left heart diseases

  • Heart failure (systolic or diastolic)

  • Valvular heart disease

 
Group 3
  • Underlying lung diseases like chronic obstructive lung disease, interstitial lung disease (ILD) and restrictive lung disease

  • Induced hypoxia due to sleep disorder, alveolar hypoventilation or chronic exposure to high altitude

 
Group 4
  • Pulmonary hypertension due to chronic thromboembolic events also known as chronic thromboembolic pulmonary hypertension (CTEPH)