Table 6. Evaluation of muscle activity in patients with propionic acidemia.
Results reported at baseline and at the conclusion of the study.
| Pt: | 1 | 2 | ||
|---|---|---|---|---|
| Hand-Held Myometry | Composite Score (lbs) | Before After |
10.85 14.7 |
12.6 12.85 |
| Time Function Test | 10 meter walk/run (sec) | Before After |
7.1 5 |
14.6 NA** |
| Time to rise from supine to stand (sec) | Before After |
3.3 4.2 |
NA** NA** |
|
| Time to climb 4 stairs (sec) | Before After |
4.3 2.7 |
12.9 14.7 |
|
| Accelerometry Tests | Average steps in 7 days | Before After |
7679 5599 |
2192 1891 |
| Average minutes of activity in 7 days | Before After |
496 485 |
247 227 |
|
| Average % of inactivity in 7 days | Before After |
65.5 66.3 |
82.8 84.21 |
*
Patient 3 was unable to complete the evaluation of muscle activity.
**
Patient 2 did not bring her walker on the final day of testing and was unable to perform these tasks.