A. Immunofluorescent staining of murine HSPB1 (mHSPB1) and
misfolded SOD1 in wild type and SOD1(G93A) mouse astrocytes. Nuclei were
visualized with DAPI. B. Percentage of wild type or SOD1(G93A)
astrocytes stained positive for mHSPB1. Cells were counted in 5 random fields of
view and expressed as the number of mHSPB1 positive cells over total cells.
C. Representative immunoblot of mHSPB1 protein levels in wild
type and SOD1(G93A) mouse astrocytes (left panel) and SOD1(G93A) astrocytes
infected with lentiviral shRNA against Hspb1. D.
Quantification of mHSPB1 immuno-staining in SOD1(G93A) astrocytes and SOD1(G93A)
astrocytes transduced with shHspb1. mHSPB1 signal intensity was
normalized to mHSPB1 signal intensity from SOD1(G93A) astrocyte lysates. Error
bars denote s.e.m. E. MN survival at day 6 of MN co-culture assay
with wild type, SOD1(G93A), SOD1(G93A) + sh Hspb1 RNA or
SOD1(G93A) + shSCRM RNA astrocytes. MN survival was normalized to counts from
MNs cultured with wild type astrocytes (N = 3 for all groups, each n was run in
triplicate). Error bars denote s.e.m. ****P<0.0001, ns,
non-significant. F. Representative images of HB9-GFP expressing MNs
(shown in black) after 6 days in co-culture with wild type astrocytes,
SOD1(G93A) astrocytes, and SOD1(G93A) astrocytes transduced with shSCRM or
shHspb1.