Table 1.
Case number | Reference | Age (years)/sex | Associated syndromes | Location | Metastasis | Treatment | N-MYC amplification | Follow-up |
---|---|---|---|---|---|---|---|---|
1 | Wahl 1943 [2] | 4/M | None | Mediastinum | Yes | Radiation | N/A | Died (8-month follow-up) |
2 | Franquemont 1994 [3] | 49/M | None | Adrenal-left | No | Surgery | N/A | No evidence of disease after 1 year |
3 | Franquemont 1994 [3] | 38/M | None | Adrenal-right | Yes | Surgery and chemoradiation | N/A | Died 3 months after diagnosis |
4 | Candanedo-Gonzalez 2001 [4] | 56/F | None | Adrenal-right | No | Surgery | N/A | Asymptomatic at 24 months post-op |
5 | Tatekawa 2006 [5] | 5/M | None | Adrenal-left | No | Surgery | N/A | Unknown |
6 | Comstock 2009 [6] | 17/M | NF1 | Adrenal-laterality unspecified | No | Unknown | Non-amplified | Alive (follow-up date unknown) |
7 | Steen 2014 [7] | 46/M | None | Adrenal-left | No | Surgery | N/A | Asymptomatic and normotensive at 6 months post-op |
8 | Current study | 57/M | NF1 | Adrenal-left | No | Surgery | Non-amplified | Asymptomatic and normotensive (6 months post-op) |
9 | Current study | 5/M | None | Adrenal-left | Yes | Surgery, chemoradiation, SCT | Amplified | Died 2 years after diagnosis |
NF 1 neurofibromatosis type 1, SCT stem cell transplant