Table 1.
Number of patients treated by participating physicians, with diagnoses
| Paediatric patients | Adult patients | |
|---|---|---|
| Patients and centres | ||
| Number of centres treating patients (n = 13) | 8 | 9 |
| Total number of patients treated (n = 1239) | 178 | 1061 |
| Patients with and without lung disease, number of patients (%) | ||
| Without lung disease | 133 (75) | 539 (51) |
| With bronchiectasis | 38 (21) | 358 (34) |
| With ‘other lung disease’ | 7 (4) | 164 (15) |
| Diagnoses | ||
| Diagnoses for all patients, number of patients (%) | ||
| CVID | 57 (32) | 798 (75) |
| XLA | 33 (19) | 42 (4) |
| SPAD | 13 (7) | 37 (3) |
| ARAG | 6 (3) | 4 (0.4) |
| Hypogammaglobulinaemia | 69 (39) | 180 (17) |
| Diagnoses for patients with progressive lung disease,* number of patients (%) | ||
| CVID | 18 (42) | 307 (80) |
| XLA | 7 (16) | 18 (5) |
| SPAD | 2 (5) | 9 (2) |
| ARAG | 2 (4) | 4 (1) |
| Hypogammaglobulinaemia | 14 (33) | 40 (12) |
ARAG = autosomal recessive agammaglobulinaemia; CVID = common variable immune deficiency; SPAD = selective or partial antibody deficiency; XLA = X‐linked agammaglobulinaemia. *Lung disease that worsens over time, including bronchiectasis and other lung disease.