Table 2.

Patient-reported rates of adherence with prophylaxis

Reference	Data source	Age	Definition of adherence	Reported adherence
31	Survey	1–18 years	>75% of prescribed infusions	58.8% adherent
32	Survey	Children and adults	>80% of prescribed infusions	73% adherent
41	VERITAS-Pro	Adolescents	Score of ≥57	30% adherent
42	Pharmacy logs	Children and adults	Days supply/days observed ≥60%	Adherence achieved 50% of the time
36	Infusion logs	Children and adults	>67% weeks of prophylaxis	Children: 26 Adults: 39
37	Infusion logs	Adults, 18–56 years	Study scoring system to rate adherence with frequency and dosage	Median adherence to frequency: 76% Median adherence to dosage: 93%
4	Randomized controlled trial, infusion logs	6 months–6 years	Not defined	Mean adherence 96%; 2 of 32 had difficulty with infusion schedule