Table 1.
Clinical Characteristics of Study Patients
| Demographics | Total=172 |
|---|---|
| Sex (female/male) | 90/82 |
| Age at diagnosis, ya | 9.0 (3.0, 13.0; range 0.08–37) |
| Age at study, ya | 15.2 (11.4, 19.4; range 4.0–46.3) |
| QTc, msa | 474 (446, 496) |
| Treatment | |
| β‐Blocker only, n | 142 (83%) |
| β‐Blocker & ICD, n | 20 (12%) |
| β‐Blocker & PPM, n | 3 (2%) |
| β‐Blocker & LCSD & ICD, n | 6 (3%) |
| LCSD & ICD, n | 1 (1%) |
| Diagnostic mechanism | |
| Family screening, n | 102 (59%) |
| Incidental findings, n | 34 (20%) |
| Syncope, n | 33 (19%) |
| Cardiac arrest, n | 3 (2%) |
ICD indicates implantable cardioverter‐defibrillator; LCSD, left cardiac sympathetic denervation; PPM, permanent pacemaker; QTc, corrected QT interval.
a
Values listed represent median (interquartile range; range).